Eccrine Angiokeratomatous Hamartoma: Report of a Case with Brief Review

Authors

  • Vijayashree Raghavan Chettinad Hospitals and Research Institute
  • Devi Subbarayan Chettinad Hospitals and Research Institute
  • Ramesh K Rao Chettinad Hospitals and Research Institute

Keywords:

Eccrine Angiokeratomatous Hamartoma, Eccrine Angiomatous Hamartoma, Solitary Angiokeratoma, CD34, SMA, Cytokeratin

Abstract

Eccrine angiokeratomatous hamartoma is a newly recognised vascular lesion of the skin, with the first case being reported only in 2006.  It has a distinctive histology with features derived from two well established vascular lesions affecting the skin: solitary angiokeratoma and eccrine angiomatous hamartoma. 

A 26 year old woman presented with a long standing painless warty lesion on her right ankle. Histological examination of the excised lesion showed a combination of two vascular lesions: superficial angiokeratoma and a deeper eccrine angiomatous hamartoma. Such a histological picture is consistent with the diagnosis of recently described eccrine angiokeratomatous hamartoma. Our case represents only second such case to be reported. Immunohistochemical analysis with CD34, smooth muscle actin and cytokeratin was done.   

Author Biographies

Vijayashree Raghavan, Chettinad Hospitals and Research Institute

Associate Professor, Department of Pathology

Devi Subbarayan, Chettinad Hospitals and Research Institute

Assistant Professor, Department of Pathology

Ramesh K Rao, Chettinad Hospitals and Research Institute

Professor and HOD, Department of Pathology

References

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Published

12-07-2015

How to Cite

1.
Raghavan V, Subbarayan D, Rao RK. Eccrine Angiokeratomatous Hamartoma: Report of a Case with Brief Review. Ann of Pathol and Lab Med [Internet]. 2015 Jul. 12 [cited 2024 Nov. 26];2(3):C159-162. Available from: http://pacificejournals.com/journal/index.php/apalm/article/view/apalm197

Issue

Section

Case Report