Primary Intradural Extramedullary Extra-OsseousEwing’s Sarcoma of Cervical Spine (C5-C7)
A Case Report and Review of Literature
DOI:
https://doi.org/10.21276/apalm.2566Keywords:
Intradural, extra-skeletal Ewing’s sarcoma, spine, nerve sheath tumorAbstract
Ewing's sarcoma is a rare aggressive tumor common in bone or skeletal component. Primary Intradural Extra-medullary Extra-Osseous Ewing sarcoma of cervical spine is extremely rare malignant neoplasm and only few cases have been reported in the literature. There is a paucity of data regarding the clinical features, natural course, pre-operative diagnosis, treatment modalities and post-operative management. Herein, we report a case of a 22-year-old man who presented with inability to walk and numbness in both lower limbs. MRI findings suggested a possibility of nerve sheath tumor but was diagnosed as Intradural Extra-skeletal Ewing sarcoma on histopathological analysis. The literature with regard to primary spinal intradural extra-skeletal Ewing sarcoma was reviewed.
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