Angiomyxoma of the Lower Eyelid with Orbital Extension: A Rare Entity and Review of Literature
DOI:
https://doi.org/10.21276/apalm.2981Keywords:
Angiomyxoma, orbital tumor, proptosis, lid tumor, Carneys complexAbstract
A 60-year-old male sought medical advice for painless progressive swelling in the left eye associated with protrusion of the eyeball and diminution of vision for the past 6 months. A computed tomography scan was done which revealed a heterogeneous lesion in the inferotemporal orbit lying close to the globe without any bony erosions or intracranial extension. Incisional biopsy revealed spindle or stellate cells in a myxoid matrix with abundant thin-walled vessels. On Immunohistochemistry, the tumour was positive for vimentin and SMA. It was negative for Desmin and S-100. A diagnosis of superficial angiomyxoma of the eyelid with orbital extension was thus made. Surgical excision under general anaesthesia was planned and the mass removed in toto. The histopathological examination of the same revealed findings similar to the incision biopsy. The patient is being followed up with no recurrences till date.
References
Steeper, T. A., & Rosai, J. Aggressive angiomyxoma of the female pelvis and perineum. The American Journal of Surgical Pathology, 1983;7(5), 463–476.
Jakobiec, F. A., Callahan, A. B., Stagner, A. M., et al. Malignant rhabdoid transformation of a longstanding, aggressive, and recurrent orbital angiomyxoma. Survey of Ophthalmology 2015;60(2):166–176.
Allen, P. W., Dymock, R. B., & MacCormac, L. B. Superficial Angiomyxomas with and without Epithelial Components. The American Journal of Surgical Pathology, 1988;12(7), 519–530.
RodrÃguez-Vásquez M, GarcÃa-Arpa M, Delgado M, et al. Angiomixoma superficial. Actas Dermosifiliogr. 2005;96(5):311–4.
Bajaj MS, Mehta M, Kashyap S, et al. Clinical and pathologic profile of angiomyxomas of the orbit. Ophthal Plast Reconstr Surg. 2011;27:76e80.
Kennedy RH, Waller RR, Carney JA. Ocular pigmented spots and eyelid myxomas. Am J Ophthalmol 1987;104:533–538.
Hidayat AA, Flint A, Marentette L, et al. Myxomas and angiomyxomas of the orbit: a clinicopathologic study of 6 cases. Ophthalmology. 2007;114:1012e9.
Yuen H. K. L, Cheuk, W. Luk, F. O. J., et al. Solitary Superficial Angiomyxoma in the Eyelid. American Journal of Ophthalmology, 2005;139(6), 1141–1142.
Mishulin, A., Lever, J. F., Porter, et al. Aggressive Glabellar Angiomyxoma with Orbital Extension. Orbit, 2012;31(5):361–36.
Pujari A, Bajaj MS, Sen S, Conjunctival angiomyxoma—rare but needs observation. Can J Ophthalmol 2018;53:60–62.
Downloads
Published
How to Cite
Issue
Section
License
Copyright (c) 2021 Sahil Agrawal, Aarush Deora, Sujeeth Modaboyina, Deepsekhar Das, Mandeep Singh Bajaj, Seema Sen
This work is licensed under a Creative Commons Attribution 4.0 International License.
Authors who publish with this journal agree to the following terms:
- Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
- Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
- Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access at http://opcit.eprints.org/oacitation-biblio.html).
