Intratesticular Rhabdomyosarcoma- A Rare Childhood Tumour

Authors

  • Hilda Fernandes Department of Pathology, Fr Muller Medical College, Mangalore, India
  • Netheya Mary Thomas Department of Pathology, Fr Muller Medical College, Mangalore, India
  • Anush Serrao Department of Pathology, Fr Muller Medical College, Mangalore, India

DOI:

https://doi.org/10.21276/apalm.3137

Keywords:

testis, embryonal, rhabdomyosarcoma

Abstract

Primary malignant of tumours of the testis are rare in children. Tumours of germ cell origin account for 60-77% of primary testicular tumors. Intrascrotal tumours of nongerm cell origin are rare. Rhabdomyosarcomas (RMS) are the commonest tumours among nongerm cell tumours. RMS are more commonly seen in paratesticular region. Pure testicular RMS are rare. A 16 yr boy was evaluated right sided testicular mass. Histopathology and immunohistochemistry confirmed it to be an anaplastic embryonal rhabdomyosarcoma. Here we report this case with a brief review of literature.

References

Dagher R and Helman L: Rhabdomyosarcoma: An overview. Oncologist 4: 34 44, 1999

Siwillis EM, Dharse NJ, Scanlan T, Ngoma M, Abraham ZS, Kahiu JW, et al.Pediatric soft tissue and bone sarcomas in Tanzania: epidemiology and clinical features. J Glob Oncol. 2019;5:1–6.

Venyo AK-G. Rhabdomyosarcoma of the testis, epididymis and spermatic cord: A review and update. Pulsus J Surg Res. 2018;2:435–41.

Ciftci A O, Bingo M, lu I K, Mehmet E. S¸ Enocak, F. Tanyel C et al. Testicular tumours in children. J paediatr Surg.2001:36;1796-81

Rudzinski E R, Anderson J R, Hawkins D S, Skapek S X, Parham D M, Teot MA. The World Health Organization Classification of Skeletal Muscle Tumors in Pediatric Rhabdomyosarcoma: A Report From the Children’s Oncology Group. Arch Pathol Lab Med. 2015 October ; 139: 1281–1287.

Kelly B, Lundon D, Rowaiye B, Daly P, Walsh K. Embryonal rhabdomyosarcoma of the testis. Canad Urol Assoc J. 2011;5:E7.

Manasseh AN, Echejoh GO, Silas OA, Tanko MN, Jegede SK, Mandong BM. Testicular embryonal rhabdomyosarcoma: A case Report. Int J Med Med Sci 2009;1:470-2.

Nasit JG, Parikh B, Trivedi P, Shah M. Primary intratesticular rhabdomyosarcoma in pediatrics. Ind J Urol. 2013;29:77.

Yi J, Zhou D A, Huo JR, Wang Y N , Ma J N. Primary intratesticular rhabdomyosarcoma: A case report and literature review. Oncol lettrs.2016;11:1016-20

Anusha G, Thanka J, D’CruzeL, Barathi G, Natarajan K, Scott JX. Paratesticular Embryonal Rhabdomyosarcoma with Lung Metastasis – A Rare Case Report. APALM 2020;7:164-7.

Parham DM, Ellison DA. Rhabdomyosarcomas in adults and children: an update. Arch Pathol Lab Med. 2006;130:1454-65

Hamilton CR, Pinkerton R, and Horwich A: The management of paratesticular rhabdomyosarcoma. Clin Radiol .1989;40: 314 –317,

Ruymann FB, Grovas AC. Progress in the diagnosis and treatment of rhabdomyosarcoma and related soft tissue sarcomas. Cancer Invest.2000;18:223–41.

Downloads

Published

31-03-2022

How to Cite

1.
Fernandes H, Thomas NM, Serrao A. Intratesticular Rhabdomyosarcoma- A Rare Childhood Tumour. Ann of Pathol and Lab Med [Internet]. 2022 Mar. 31 [cited 2024 Dec. 22];9(3):C24-27. Available from: https://pacificejournals.com/journal/index.php/apalm/article/view/3137

Issue

Section

Case Report