Cutaneous Rosai-Dorfman Disease – A Case Report and Review of Literature

Authors

  • Shalu Thomas Department of Pathology Believers Church Medical College and Hospital, Thiruvalla, Kerala
  • Dahlia Joseph Department of Pathology Believers Church Medical College and Hospital, Thiruvalla, Kerala
  • Renny Napolean Department of Surgery, Believers Church Medical College and Hospital, Thiruvalla, Kerala
  • Elizabeth Joseph Department of Pathology Believers Church Medical College and Hospital, Thiruvalla, Kerala

DOI:

https://doi.org/10.21276/apalm.3140

Keywords:

Cutaneous, Rosai-Dorfman disease, Emperipolesis, S-100

Abstract

Rosai–Dorfman disease (RDD), or Sinus Histiocytosis with Massive Lymphadenopathy (SHML) is a self-limiting, rare benign proliferative disorder of histiocytes in the lymph nodes with occasional extra-nodal involvement of the skin. Isolated Cutaneous Rosai-Dorfman disease(C-RDD) without node involvement is an exceedingly rare occurrence. Despite its unique characteristics, the diagnosis of Cutaneous Rosai Dorfman disease is hampered by its variable clinical presentation, misleading histopathological patterns, and the absence of lymphadenopathy. Herein we present a case report of Cutaneous Rosai-Dorfman disease without any lymph node involvement.

References

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Published

04-05-2022

How to Cite

1.
Thomas S, Joseph D, Napolean R, Joseph E. Cutaneous Rosai-Dorfman Disease – A Case Report and Review of Literature. Ann of Pathol and Lab Med [Internet]. 2022 May 4 [cited 2024 Nov. 19];9(4):C34-37. Available from: https://pacificejournals.com/journal/index.php/apalm/article/view/3140

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Section

Case Report