High Grade Appendiceal Mucinous Neoplasm Presenting as Intussusception In an Elderly Female-A Case Report
DOI:
https://doi.org/10.21276/apalm.3225Keywords:
Appendiceal mucinous tumors, intussusception, high grade, AMN, HAMNAbstract
Introduction: Appendiceal mucinous neoplasms (AMNs) are rare and account for 1% of gastrointestinal neoplasms and the diagnosis is mostly incidental. In spite of advances in the understanding of AMNs and their association with peritoneal disease, AMNs are still confusing entities in respect to their diagnosis and treatment alike.
Case Report: We report a case of a 51year old female who presented with abdominal pain and vomiting and was diagnosed as ileo-colic intussusception on ultrasonography and CECT abdomen. Histopathological examination of right hemicolectomy specimen revealed a high grade appendicular mucinous neoplasm with low grade areas. The peri-appendiceal mucin deposition forming a mass in the cecum at the base of appendix was the lead point for intussusception in this case. No features of pseudomyxoma peritonei was seen in this case. This patient is well after 18 months of follow up period.
Conclusion: Appendiceal mucinous neoplasms are rare and diagnosis is often difficult as presentation is mostly non-specific. Hence, awareness and further classification of these tumours is essential for diagnosis, determining the risk of recurrence and malignancy and also prognostication.
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Copyright (c) 2022 Manjari SKVSK, Mark Ruth Prasanna, T Satya Prakash Venkatachalam
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