A Case of Primary Intestinal Lymphangiectasia

Authors

  • Rajshri P Damle Assistant professor Department of Pathology ACPM Medical college Dhule 424001
  • Kishor H Suryawanshi
  • N V Dravid
  • D V Newadkar

Keywords:

Intestinal lymphangiectasia, Diarrhea, Edema

Abstract

Primary intestinal lymphangiectasia (PIL) is an uncommon disorder and important cause of protein losing enteropathy due to congenital malformation or obstruction of intestinal lymphatic drainage. No accurate serological or radiological tests available for the diagnosis of intestinal lymphangiectasia. Endoscopy and biopsy are currently the only diagnostic modality with certainty. Hence histopathological examination is the gold standard for the diagnosis of intestinal lymphangiectasia which shows dilated intestinal lymphatics with broadened villi of the small bowel. Herein we report a case of intestinal lymphangiectasia in a 4-year-male child presented with chronic diarrhea and edema. Patient was treated by resection of small intestine and postoperatively patient showed improvement with small bowel movements and disappearance of edema.

References

1. Waldmann TA, Steinfeld JL, Dutcher TF, Davidson JD, Gordon RS Jr. The role of the gastrointestinal system in “idiopathic hypoproteinemia”. Gastroenterology 1961; 41:197-207

2. Fang YH, Zhang BL, Wu JG, Chen CX. A primary intestinal lymphangiectasia patient diagnosed by capsule endoscopy and confirmed at surgery: A case report. World J Gastroenterol 2007;13: 2263-5.

3. Freeman HJ, Nimmo M. Intestinal lymphangiectasia in adults. World J Gastrointest Oncol 2011; 3:19-23.

4. Vignes S, Bellanger J. Primary intestinal lymphangiectasia (Waldmann’s disease). Orphanet J Rare Dis 2008; 3:5

5. Mistilis SP, Skyring AP, Stephen DD. Intestinal lymphangiectasia mechanism of enteric loss of plasma protein and fat. Lancet 1965; 1:77-9.

6. Wen J, Tang Q, Wu J, Wang Y, Cai W. Primary intestinal lymphangiectasia: Four case reports and a review of the literature. Dig Dis Sci 2010;55:3466-72

7. Hauser B, Moreels T, Urbain D, Van Marck V, Pletincx M, Devreker T, et al. Intestinal lymphangiectasia. J Pediatr Gastroenterol Nutr. 2009 ;48(2):125.

8. Levine C. Primary disorders of the lymphatic vessels – A unified concept. J Pediatr Surg 1989; 24: 233-24.

Downloads

Published

28-10-2015

How to Cite

1.
Damle RP, Suryawanshi KH, Dravid NV, Newadkar DV. A Case of Primary Intestinal Lymphangiectasia. Ann of Pathol and Lab Med [Internet]. 2015 Oct. 28 [cited 2024 Nov. 7];2(4):C248-251. Available from: https://pacificejournals.com/journal/index.php/apalm/article/view/apalm339

Issue

Vol. 2 No. 4 (2015)

Section

Case Report

License

Copyright (c) 2015 Rajshri P Damle, Kishor H Suryawanshi, N V Dravid, D V Newadkar

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Authors who publish with this journal agree to the following terms:

  1. Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
  2. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
  3. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access at http://opcit.eprints.org/oacitation-biblio.html).