Primary Systemic Amyloidosis: A Case Report

Authors

  • Tanima Dwivedi Post Graduate, Department of Pathology, KLE University’s J.N. Medical College, Belgaum, Karnataka(India)-590010
  • Ramesh Chavan Professor, Department of Pathology, KLE University’s J.N.Medical college, Belgaum, Karnataka(India)-590010

Keywords:

primary systemic amyloidosis, Idiopathic, plasma cell dyscrasia, AL amyloidosis

Abstract

Primary systemic amyloidosis is a rare entity. We report a case of primary systemic primary amyloidosis, an elderly male presented with generalized weakness since 6 months. Clinical examination revealed typical waxy lesions in the periorbital area with macroglossia. Serum electrophoresis was normal, however, bone marrow examination showed increased plasma cell with a good number of both binucleated and immature plasma cells. Diagnosis was confirmed by skin biopsy using haemotoxylin & eosin staining and congo red staining. Polarised microscopy was not done because of unavailability. We present the myriad manifestations of this uncommon disease entity.

Author Biographies

Tanima Dwivedi, Post Graduate, Department of Pathology, KLE University’s J.N. Medical College, Belgaum, Karnataka(India)-590010

post graduate, pathology

Ramesh Chavan, Professor, Department of Pathology, KLE University’s J.N.Medical college, Belgaum, Karnataka(India)-590010

Professor, Department of Pathology, KLE University’s J.N.Medical College,Belagavi,Karnataka(India)-590010

 

References

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Published

25-02-2016

How to Cite

1.
Dwivedi T, Chavan R. Primary Systemic Amyloidosis: A Case Report. Ann of Pathol and Lab Med [Internet]. 2016 Feb. 25 [cited 2024 Nov. 23];3(1):C40-43. Available from: https://pacificejournals.com/journal/index.php/apalm/article/view/apalm446

Issue

Vol. 3 No. 1 (2016)

Section

Case Report

License

Copyright (c) 2016 Tanima Dwivedi, Ramesh Chavan

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