A Rare Case of Paratesticular Rhabdomyosarcoma in an Infant: Surgical and Pathologic Perspectives
DOI:
https://doi.org/10.21276/apalm.3991Keywords:
rhabdomyosarcoma, paratesticular, scrotal sac, immunohistochemistryAbstract
Background: Paratesticular spindle cell rhabdomyosarcoma is an extremely rare soft tissue sarcoma, accounting for only about 5% of all paratesticular rhabdomyosarcomas. It primarily affects children and adolescents, with very few cases reported in infants.
Case Summary: A 5-month-old baby presented with a painless mass in left scrotal sac, detected incidentally during a routine vaccination visit. Clinical examination revealed a firm, non-tender mass inseparable from the left testis. High inguinal orchidectomy was performed and the specimen was sent for histopathological examination. Histopathology along with immunohistochemistry established the diagnosis of spindle cell rhabdomyosarcoma of the paratesticular region.
Conclusion: Paratesticular spindle cell rhabdomyosarcoma, though rare in infancy, should be considered in the differential diagnosis of painless scrotal masses. Early detection due to superficial location, complete surgical resection and adjuvant VAC chemotherapy offers a favourable prognosis. However, long-term follow-up is essential.
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Copyright (c) 2026 Madhuri Sethia, Reena Tomar, Sujoy Neogi, Lekshmi Satheesh
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