A rare case of Juvenile Fibromatosis infiltrating neck subcutis in a 3-year old girl

Authors

  • Amit Kumar Senior Resident Department of Pathology Mahavir Cancer Institute And Research Centre, Patna (Bihar)
  • Rakesh Mehra Consultant Radiologist Department of Radiology Mahavir Cancer Institute And Research Centre, Patna (Bihar)
  • Tanushree Narain DNB Resident Department of Pathology Mahavir Cancer Institute And Research Centre, Patna (Bihar)
  • Neha Garg DNB Resident Department of Pathology Mahavir Cancer Institute And Research Centre, Patna (Bihar)
  • Pallavi Agrawal Consultant Pathologist M.D., DNB, PDCC Department of Pathology Mahavir Cancer Institute And Research Centre, Patna (Bihar)

Keywords:

Juvenile, Fibromatosis, neck, submandibular

Abstract

Background: Fibromatosis is a rare benign tumor of fibro-myofibroblastic origin. This non-metastasizing tumor has high potential to locally invade and recur after surgical excision. Since 1950, only 99 cases of fibromatosis of head and neck in pediatric age-group are reported in the literature. We present the 100th case in this category.

Case-report: A three year old girl presented with a right sided neck mass progressively increasing in size since one year. On imaging the tumor was found extending from submandibular to supraclavicular region, which on incisional biopsy showed features consistent with the diagnosis of Juvenile Fibromatosis. Histologically, it may be confused with other entities under broad diagnostic category ‘fibromatoses’, but immuno-histochemical analysis confirmed the diagnosis. Patient underwent wide local excision and was followed-up for two years with no features of recurrence.

Conclusion: A rare and interesting tumor of pediatric age group with high tendency to recur after surgical excision. But surgical resection with tumor free margins prognostically decreases the chance of recurrence.

References

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Published

08-05-2016

How to Cite

1.
Kumar A, Mehra R, Narain T, Garg N, Agrawal P. A rare case of Juvenile Fibromatosis infiltrating neck subcutis in a 3-year old girl. Ann of Pathol and Lab Med [Internet]. 2016 May 8 [cited 2024 Nov. 19];3(2):C78-81. Available from: https://pacificejournals.com/journal/index.php/apalm/article/view/APALM557

Issue

Vol. 3 No. 2 (2016)

Section

Case Report

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Copyright (c) 2016 Amit Kumar, Rakesh Mehra, Tanushree Narain, Neha Garg, Pallavi Agrawal

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