Angiomyomatous Hamartoma: a true lesion or a vascular compensatory hyperplasia with muscularization? : An interesting case report

Authors

  • Rakesh K Gupta G B Pant Institute of Postgraduate Medical Education and Research, New Delhi
  • Kavita Gaur G B Pant Institute of Postgraduate Medical Education and Research, New Delhi
  • R K Jindal Maulana Azad Medical College, Bahadur Shah Zafar Marg, New Delhi
  • Ravindra Kumar Saran G B Pant Institute of Postgraduate Medical Education and Research, New Delhi
  • Sachin Agrawal G B Pant Institute of Postgraduate Medical Education and Research, New Delhi

Keywords:

Angiomyomatous, hamartoma, lymph node, lymphedema

Abstract

Angiomyomatous hamartoma is a rare entity of unknown etiology preferentially involving   lymph nodes of the inguinal region. We report a case of 20-year-old young male presenting with unilateral lower limb lymphedema. Doppler study of the limb revealed venous flow in the node. Histopathology of the lymph node showed a peculiar replacement of normal hilar anatomy by haphazard conglomerate of thick walled vessels containing red blood cells and lymphocytes. The present report explores the pathogenesis of angiomyomatous hamartoma with review of literature.

Author Biographies

Rakesh K Gupta, G B Pant Institute of Postgraduate Medical Education and Research, New Delhi

Pathology

Kavita Gaur, G B Pant Institute of Postgraduate Medical Education and Research, New Delhi

Pathology

R K Jindal, Maulana Azad Medical College, Bahadur Shah Zafar Marg, New Delhi

Surgery

Ravindra Kumar Saran, G B Pant Institute of Postgraduate Medical Education and Research, New Delhi

Professor

Department of Pathology

Sachin Agrawal, G B Pant Institute of Postgraduate Medical Education and Research, New Delhi

Radiology

References

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Published

02-05-2016

How to Cite

1.
Gupta RK, Gaur K, Jindal RK, Saran RK, Agrawal S. Angiomyomatous Hamartoma: a true lesion or a vascular compensatory hyperplasia with muscularization? : An interesting case report. Ann of Pathol and Lab Med [Internet]. 2016 May 2 [cited 2024 Nov. 19];3(2):C56-59. Available from: https://pacificejournals.com/journal/index.php/apalm/article/view/apalm510

Issue

Vol. 3 No. 2 (2016)

Section

Case Report

License

Copyright (c) 2016 Rakesh K Gupta, Kavita Gaur, R K Jindal, Ravindra Kumar Saran, Sachin Agrawal

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