Monomorphic Epitheliotropic Intestinal T-Cell Lymphoma Mimicking Benign Lymphocytic Infiltrates: A Pathologic Masquerade

Kuljeet Kaur; Maitrayee Roy; Vishesh Dhawan; Ayushi Kediya

doi:10.21276/apalm.3712

Authors

Kuljeet Kaur Department of Pathology, Maharishi Markandeshwar Centre of Medical Sciences and Research, Maharishi Markandeshwar Deemed to be University, Sadopur-Ambala, Haryana, India
Maitrayee Roy Department of Pathology, Maharishi Markandeshwar Institute of Medical Sciences and Research, Maharishi Markandeshwar Deemed to be University, Mullana-Ambala, Haryana, India
Vishesh Dhawan Department of Pathology, Maharishi Markandeshwar Institute of Medical Sciences and Research, Maharishi Markandeshwar Deemed to be University, Mullana-Ambala, Haryana, India
Ayushi Kediya Department of Pathology, Maharishi Markandeshwar Institute of Medical Sciences and Research, Maharishi Markandeshwar Deemed to be University, Mullana-Ambala, Haryana, India

DOI:

https://doi.org/10.21276/apalm.3712

Keywords:

monomorphic epitheliotropic intestinal t-cell lymphoma, immunohistochemistry, lymphoma

Abstract

Monomorphic Epitheliotropic Intestinal T-cell Lymphoma (MEITL) is a rare aggressive T-cell lymphoma mostly found in Asia. It accounts for less than 5% of primary gastrointestinal malignant lymphomas, is rapidly progressing, and has a poor prognosis with a median survival of 7 months. The relatively small size of atypical cells coupled with brisk cryptitis can result in a misdiagnosis of lymphocytic proctocolitis. A strong index of suspicion is required to employ an appropriate IHC panel for this diagnosis. In this case report, we want to describe a 50-year-old patient who presented with chronic lower gastrointestinal symptoms and was diagnosed with MEITL involving the large intestine and ileum.

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